Haemophagocytic lymphohistiocytosis (HLH): case series in tertiary referral hospital over three years.
نویسندگان
چکیده
Haemophagocytic lymphohistiocytosis (HLH) is a rare but potentially fatal disease of normal but overactive histiocytes and lymphocytes that commonly appears in infancy, although it has been seen in all age groups. We are reporting a series of 5 cases of HLH in young adult and paediatric patients identified over three years.
منابع مشابه
Non-familial haemophagocytic lymphohistiocytosis in children.
Haemophagocytic Lymphohistiocytosis (HLH) is a rare clinical illness with a high mortality. There are reported effective treatment and a favourable outcome if diagnosed early. Five cases of childhood non-familial HLH seen over a 3 year period in our hospital are presented. The diagnosis was not suspected in the referring hospitals even after a bone marrow biopsy examination in two cases. Delay ...
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ورودعنوان ژورنال:
- The Journal of the Association of Physicians of India
دوره 61 11 شماره
صفحات -
تاریخ انتشار 2013